Case for diagnosis

Case for diagnosis

Blog Article

Degos disease, also known Drawing as malignant atrophic papulosis, is a rare occlusive vasculopathy of unknown etiology characterized by infarcts in the dermis, gastrointestinal tract, central nervous system, and other organs.It is characterized by papules, which become umbilicated and evolve with a depressed porcelain-white central area, with an erythematous halo with telangiectasias.Histological findings include LADIES SKIRTS SUIT wedge-shaped dermoepidermal necrosis and blood vessel thrombosis.Approximately 50-60% of patients with systemic symptoms die within 2-3 years, most due to gastrointestinal perforation.We report a typical case, with lethal outcome, in a 45-year-old woman.